{"id":2654,"date":"2019-09-14T13:54:36","date_gmt":"2019-09-14T13:54:36","guid":{"rendered":"https:\/\/jfim.org\/es\/?p=2654"},"modified":"2019-09-18T17:27:57","modified_gmt":"2019-09-18T17:27:57","slug":"miocardiopatia-hipertrofica-como-no-cometer-errores","status":"publish","type":"post","link":"https:\/\/jfim.org\/es\/miocardiopatia-hipertrofica-como-no-cometer-errores\/","title":{"rendered":"Miocardiopat\u00eda hipertrof\u00edca, como no cometer errores"},"content":{"rendered":"<div id=\"dslc-main\">\r\n\t\t\t<div  class=\"dslc-modules-section \" style=\"background-color:rgba(230, 230, 230, 0);border-color:rgb(230, 230, 230);border-width:1px;border-right-style: hidden; border-bottom-style: hidden; border-left-style: hidden; \" data-section-id=\"f8f563d7d45\">\r\n\t\t\t\t\r\n\t\t\t\t\r\n\t\t\t\t<div class=\"dslc-modules-section-wrapper dslc-clearfix\"><div  class=\"dslc-modules-area dslc-col dslc-12-col dslc-last-col\" data-size=\"12\" data-valign=\"\" data-modules-area-id=\"\" ><style type=\"text\/css\" id=\"dslca-modules-area-\"><\/style>\r\n\t\t<div id=\"dslc-module-276\" class=\"dslc-module-front dslc-module-DSLC_TP_Title dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-12-col dslc-last-col  dslc-module-handle-like-regular \" data-module-id=\"276\" data-module=\"DSLC_TP_Title\" data-dslc-module-size=\"12\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\r\n\t<div class=\"dslc-tp-title\">\r\n\t\t\t\t\t<div class=\"dslc-tp-title\"><h1>Miocardiopat\u00eda hipertrof\u00edca, como no cometer errores<\/h1><\/div>\r\n\t\t\t<\/div>\r\n\r\n\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-277\" class=\"dslc-module-front dslc-module-DSLC_TP_Meta dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-9-col  dslc-module-handle-like-regular \" data-module-id=\"277\" data-module=\"DSLC_TP_Meta\" data-dslc-module-size=\"9\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\r\n\t\t\t\t<div class=\"dslc-tp-meta dslc-tp-meta-horizontal\">\r\n\t\t\t\t\t<ul class=\"dslc-clearfix\">\r\n\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t<li>September 14, 2019<\/li>\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<li><a href=\"https:\/\/jfim.org\/es\/category\/bueno-aires\/\">Bueno Aires<\/a>, <a href=\"https:\/\/jfim.org\/es\/category\/bueno-aires\/sessions\/\">Sessions<\/a><\/li>\t\t\t\t\t\t\t\t\t\t\t\t\t\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t<\/ul>\r\n\t\t\t\t<\/div>\r\n\r\n\t\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-278\" class=\"dslc-module-front dslc-module-DSLC_TP_Downloads_Button dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-3-col dslc-last-col  dslc-module-handle-like-regular downloadpdf\" data-module-id=\"278\" data-module=\"DSLC_TP_Downloads_Button\" data-dslc-module-size=\"3\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\r\n\t\t\t\t<div class=\"dslc-tp-download-button\">\r\n\t\t\t\t\t\t\t\t\t\t<a target=\"_blank\" class=\"dslc-download-count-hook\" data-post-id=\"2654\" href=\"\" download>\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"dslc-icon dslc-icon-\"><\/span>\t\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span>DOWNLOAD PDF<\/span>\r\n\t\t\t\t\t\t\t\t\t\t\t<\/a>\r\n\t\t\t\t<\/div><!-- .dslc-download-button -->\r\n\r\n\t\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-285\" class=\"dslc-module-front dslc-module-DSLC_Separator dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-1-col  dslc-module-handle-like-regular \" data-module-id=\"285\" data-module=\"DSLC_Separator\" data-dslc-module-size=\"1\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\t\t\t<div class=\"dslc-separator-wrapper\">\n\t\t\t\t<div class=\"dslc-separator dslc-separator-style-invisible\">\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<div><\/div>\n\t\t\t<\/div><!-- .dslc-separator-wrapper -->\n\t\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-279\" class=\"dslc-module-front dslc-module-DSLC_TP_Content dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-10-col  dslc-module-handle-like-regular elpframe\" data-module-id=\"279\" data-module=\"DSLC_TP_Content\" data-dslc-module-size=\"10\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\t\t<div class=\"dslc-tp-content\">\r\n\t\t\t<p style=\"text-align: center;\"><iframe id=\"elpframe\" src=\"https:\/\/jfim.org\/webinar\/ES\/draogonetti-ba-2017\/index.html\" width=\"100%\" height=\"900px\" allowfullscreen=\"allowfullscreen\"><span data-mce-type=\"bookmark\" style=\"display: inline-block; width: 0px; overflow: hidden; line-height: 0;\" class=\"mce_SELRES_start\">\ufeff<\/span><\/iframe><\/p>\r\n<strong><em>Miocardiopat\u00edas Infiltrativas que simulan la MCP hipertr\u00f3fica<\/em><\/strong>\r\n\r\n\u00bfPor qu\u00e9 diferenciarlas? Importancia de arribar a un diagn\u00f3stico certero\r\n\r\n&nbsp;\r\n\r\nLa MCPH es una enfermedad hereditaria que se caracteriza por una gran variabilidad cl\u00ednica, morfol\u00f3gica y gen\u00e9tica y su importancia radica en que es la principal causa de MS en individuos j\u00f3venes, sin otra patolog\u00eda\u00a0asociada.\r\n\r\nEs por \u00e9sto que se desaconseja la pr\u00e1ctica competitiva en los atletas j\u00f3venes portadores de la enfermedad. Numerosos estudios han intentado identificar el mayor riesgo y su diferenciaci\u00f3n de otras causas que puedan SIMULARLA (Fenocopias) dentro de las cuales se destacan la Amiloidosis y la Enf Fabry.\r\n\r\nLa resonancia se presenta como un M\u00e9todo inocuo, no invasivo, indoloro que permite valorar espesores parietales, Vol\u00famenes y funci\u00f3n ventricular(hoy en d\u00eda el Gold Standart)\r\n\r\n&nbsp;\r\n\r\n<em>1- Amiloidosis card\u00edaca:<\/em> es el Prototipo de enfermedad por dep\u00f3sito que ocasiona engrosamiento mioc\u00e1rdico difuso llevando a una MCPH con fracci\u00f3n de eyecci\u00f3n preservada. La afectaci\u00f3n card\u00edaca es la causa m\u00e1s frecuente de morbimortalidad y la RM puede colaborar al dg demostrando en tiempos de realce <em>temprano (3\u2019 post inyecci\u00f3n) anulaci\u00f3n del pool sangu\u00edneo<\/em> y<em> realce <\/em>sub-endoc\u00e1rdico difuso, sin corresponder a un territorio coronario<em>.<\/em>\r\n\r\n<em>2 - Enfermedad de Fabry<\/em>: Es una enfermedad gen\u00e9tica asociada al d\u00e9ficit de galactosidasa A que provoca ac\u00famulo de glucoesfingol\u00edpidos en numerosos \u00f3rganos.\r\n\r\nEn este caso la RM tiene la capacidad de detectar un Realce Mioc\u00e1rdico Tard\u00edo caracter\u00edstico de tipo intramioc\u00e1rdico que se localiza en el segmento infero-lateral-basal y respeta el sub endocardio.\r\n\r\n&nbsp;\r\n\r\nDg diferencial de FENOCOPIAS. MCPH- Enf de Fabry \u2013 Amiloidosis\r\n\r\nRecordemos que hablamos de enfermedades raras, debilitantes, graves y progresivas, de caracter\u00edsticas morfol\u00f3gicas muy variables. Donde la afectaci\u00f3n card\u00edaca est\u00e1 presente pr\u00e1cticamente en todos los pacientes y su gravedad aumenta con el transcurso del tiempo.\r\n\r\nPor eso la RMC es un m\u00e9todo que nos acerca al diagn\u00f3stico, estratificaci\u00f3n y pron\u00f3stico, para as\u00ed arribar al tratamiento espec\u00edfico.\r\n\r\n&nbsp;\t\t<\/div>\r\n\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-280\" class=\"dslc-module-front dslc-module-DSLC_TP_Comments dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-12-col  dslc-module-handle-like-regular \" data-module-id=\"280\" data-module=\"DSLC_TP_Comments\" data-dslc-module-size=\"12\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\t\t\r\n\t\t\t<div class=\"dslc-tp-comments\" id=\"comments\">\r\n\r\n\t\t\t\t\r\n\t\t\t\t\t\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t\t<ol class=\"comments clean-list\">\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/ol><!-- .commentlist -->\r\n\r\n\t\t\t\t\t\t\r\n\t\t\t\t\t\r\n\t\t\t\t\t\r\n\t\t\t\t\r\n\t\t\t<\/div><!-- dslc-tp-comments -->\r\n\r\n\t\t\r\n\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-281\" class=\"dslc-module-front dslc-module-DSLC_TP_Comments_Form dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-12-col  dslc-module-handle-like-regular \" data-module-id=\"281\" data-module=\"DSLC_TP_Comments_Form\" data-dslc-module-size=\"12\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\t\t\r\n\t\t<div class=\"dslc-tp-comment-form\">\r\n\r\n\t\t\t\t<div id=\"respond\" class=\"comment-respond\">\n\t\t<h3 id=\"reply-title\" class=\"comment-reply-title\">Leave a Comment <small><a rel=\"nofollow\" id=\"cancel-comment-reply-link\" href=\"\/es\/wp-json\/wp\/v2\/posts\/2654#respond\" style=\"display:none;\">cancel<\/a><\/small><\/h3><p class=\"must-log-in\">You must be <a href=\"https:\/\/jfim.org\/es\/wp-login.php?redirect_to=https%3A%2F%2Fjfim.org%2Fes%2Fmiocardiopatia-hipertrofica-como-no-cometer-errores%2F\">logged in<\/a> to post a comment.<\/p>\t<\/div><!-- #respond -->\n\t\r\n\t\t<\/div><!-- dslc-tp-comment-form -->\r\n\r\n\t\t\t\t<style type=\"text\/css\">\r\n\t\t\t.dslc-tp-comment-form input[type=text]::-moz-placeholder, .dslc-tp-comment-form input[type=url]::-moz-placeholder, .dslc-tp-comment-form input[type=email]::-moz-placeholder, .dslc-tp-comment-form textarea::-moz-placeholder {\r\n\t\t\t\tcolor: #4d4d4d;\r\n\t\t\t}\r\n\t\t\t.dslc-tp-comment-form input[type=text]::-webkit-input-placeholder, .dslc-tp-comment-form input[type=url]::-webkit-input-placeholder, .dslc-tp-comment-form input[type=email]::-webkit-input-placeholder, .dslc-tp-comment-form textarea::-webkit-input-placeholder {\r\n\t\t\t\tcolor: #4d4d4d;\r\n\t\t\t}\r\n\t\t\t.dslc-tp-comment-form input[type=text]:-ms-input-placeholder, .dslc-tp-comment-form input[type=url]:-ms-input-placeholder, .dslc-tp-comment-form input[type=email]:-ms-input-placeholder, .dslc-tp-comment-form textarea:-ms-input-placeholder {\r\n\t\t\t\tcolor: #4d4d4d;\r\n\t\t\t}\r\n\t\t<\/style>\r\n\t\t\r\n\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t<\/div><\/div><\/div>\r\n\t\t\t<div id=\"logbox\" class=\"dslc-modules-section \" style=\"\" data-section-id=\"0fa68dc2d02\">\r\n\t\t\t\t\r\n\t\t\t\t\r\n\t\t\t\t<div class=\"dslc-modules-section-wrapper dslc-clearfix\"><div  class=\"dslc-modules-area dslc-col dslc-12-col dslc-last-col\" data-size=\"12\" data-valign=\"\" data-modules-area-id=\"\" ><style type=\"text\/css\" id=\"dslca-modules-area-\"><\/style>\r\n\t\t<div id=\"dslc-module-282\" class=\"dslc-module-front dslc-module-DSLC_Text_Simple dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-12-col dslc-last-col  dslc-module-handle-like-regular \" data-module-id=\"282\" data-module=\"DSLC_Text_Simple\" data-dslc-module-size=\"12\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"0\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\n\t\t<div class=\"dslc-text-module-content\">\n\t\t\t<h3 style=\"text-align: center;\" data-mce-style=\"text-align: center;\">To download this content, you have to be logged in or become a member.<\/h3>\t\t<\/div>\n\n\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-283\" class=\"dslc-module-front dslc-module-DSLC_Button dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-6-col  dslc-module-handle-like-regular \" data-module-id=\"283\" data-module=\"DSLC_Button\" data-dslc-module-size=\"6\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\r\n\t\t\t<div class=\"dslc-button\">\r\n\t\t\t\t\t\t\t\t\t<a href=\"https:\/\/jfim.org\/login\" target=\"_blank\"  onClick=\"\" class=\"\">\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"dslc-icon dslc-icon-user-md\"><\/span>\t\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span>LOGIN<\/span>\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/a>\r\n\t\t\t\t\t\t\t<\/div><!-- .dslc-button -->\r\n\r\n\r\n\t\t\t\t\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t\r\n\t\t<div id=\"dslc-module-284\" class=\"dslc-module-front dslc-module-DSLC_Button dslc-in-viewport-check dslc-in-viewport-anim-none  dslc-col dslc-6-col dslc-last-col  dslc-module-handle-like-regular \" data-module-id=\"284\" data-module=\"DSLC_Button\" data-dslc-module-size=\"6\" data-dslc-anim=\"none\" data-dslc-anim-delay=\"\" data-dslc-anim-duration=\"650\"  data-dslc-anim-easing=\"ease\" data-dslc-preset=\"none\" >\r\n\r\n\t\t\t\r\n\t\t\t\r\n\t\t\r\n\t\t\t<div class=\"dslc-button\">\r\n\t\t\t\t\t\t\t\t\t<a href=\"https:\/\/jfim.org\/subscrib\" target=\"_blank\"  onClick=\"\" class=\"\">\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"dslc-icon dslc-icon-user-plus\"><\/span>\t\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span>BECOME A MEMBER<\/span>\r\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/a>\r\n\t\t\t\t\t\t\t<\/div><!-- .dslc-button -->\r\n\r\n\r\n\t\t\t\t\t\t\r\n\t\t\t\t<\/div><!-- .dslc-module -->\r\n\t\t<\/div><\/div><\/div><\/div><input type=\"hidden\" id=\"dslca-post-data-thumb\" value=\"https:\/\/jfim.org\/es\/wp-content\/uploads\/sites\/3\/2019\/09\/Diapositive04.jpg\" \/>","protected":false},"excerpt":{"rendered":"Laura DRAGONETTI<br \/>\r\n\r\nBuenos Aires, Argentina<br \/>\r\n\r\nSession, Buenos Aires, Nov 2017","protected":false},"author":1,"featured_media":2655,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[2,6],"tags":[10,13,11,12],"class_list":["post-2654","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-bueno-aires","category-sessions","tag-cardiac","tag-dragonetti","tag-thoracic","tag-vascular"],"_links":{"self":[{"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/posts\/2654","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/comments?post=2654"}],"version-history":[{"count":2,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/posts\/2654\/revisions"}],"predecessor-version":[{"id":2658,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/posts\/2654\/revisions\/2658"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/media\/2655"}],"wp:attachment":[{"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/media?parent=2654"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/categories?post=2654"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/jfim.org\/es\/wp-json\/wp\/v2\/tags?post=2654"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}